Immuno-reconstitution by thymic transplant in DiGeorge's syndrome.
نویسندگان
چکیده
Persistent hypocalcaemic tetany in a breast-fed neonate made us suspect DiGeorge's syndrome, particularly as the baby had an abnormal facies, and a ventricular septal defect. Immuno-reconstitution was successfully achieved by thymic transplant. Evidence of immuno-reconstitution on the basis of the histology of the post-transplant thymus has not been previously recorded.
منابع مشابه
DiGeorge's syndrome
DiGeorge's syndrome results from an interference in embryogenesis between the sixth and tenth week of intrauterine life, involving the third and fourth branchial arches; the first antasecond arches are often and the sixth arch occasionally involved. The association of congenital absence of the thymus with seizures in the newborn and abnormal third and fourth pharyngeal pouch development was rec...
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ورودعنوان ژورنال:
- Postgraduate medical journal
دوره 60 706 شماره
صفحات -
تاریخ انتشار 1984